Successful Palliation in Monochorionic Twins with Hypoplastic Left Heart Syndrome
نویسندگان
چکیده
Hypoplastic left heart syndrome is a congenital disease which accounts for 8% of all defects. Twin pregnancies have significantly higher risk structural than singleton ones, however the concordance rate has been found to be relatively low, even in monochorionic pregnancies. We describe here favorable evolution monochorionic, diamniotic, twin pregnancy both fetuses were diagnosed with hypoplastic by antenatal echocardiography. The present report suggests that at least some cases there may genetic contribution etiology. fetal diagnosis was imperative good postnatal outcome.
منابع مشابه
Hypoplastic left heart syndrome
Hypoplastic left heart syndrome (HLHS) refers to the abnormal development of the left-sided cardiac structures, resulting in obstruction to blood flow from the left ventricular outflow tract. In addition, the syndrome includes underdevelopment of the left ventricle, aorta, and aortic arch, as well as mitral atresia or stenosis. HLHS has been reported to occur in approximately 0.016 to 0.036% of...
متن کاملHypoplastic left-heart syndrome.
Hypoplastic left heart syndrome may be accurately diagnosed during fetal life. Prenatal diagnosis provides the opportunity for parents to make an informed choice about their options, including surgery, nonintervention postnatally or termination of pregnancy. Short to medium term survival continues to improve for a condition that was previously invariably lethal. There continues to be a signific...
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Hypoplastic left heart syndrome is a severe form of congenital heart disease that results in single-ventricle physiology. Although surgical palliation in infants with this syndrome is widely agreed on in practice, variation occurs in both surgical and medical management. Perinatal factors that affect preoperative management include the subtype of the syndrome and the patient's birth weight, ges...
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In the last decade the hybrid procedure has emerged as an alternative stage I palliation in neonates with hypoplastic left heart syndrome (HLHS). This review discusses the historical aspect, surgical and interventional techniques, current outcomes and future direction of this procedure. Hybrid palliation yields equivalent but not superior stage I palliation survival and comparable 1-year surviv...
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ژورنال
عنوان ژورنال: Cardiology research and reports
سال: 2022
ISSN: ['2692-9759']
DOI: https://doi.org/10.31579/2692-9759/047